An experience of complete correction (CC) of the complex congenital heart disease (CHD), pulmonary atresia (PA) with ventricular septal defect (VSD) type A in 55 patients of age from 5.5 to 312 мonths (mean 102.0±84.4) is presented in article. Among them 52 patients had been performed CC after palliative procedures, under conditions of artificial circulation, deep hypothermia 22–25 °С. After right ventriculotomy of right ventricular outflow tract (RVOT) muscle bundles are resected, VSD patch closure, connection between the right ventricle and the pulmonary artery was created. 43 patients were made transannular patch, 23 from them — with a monocusp method of Loma Linda MC CA. 12 patients had insertion of artificial of trunk pulmonary artery as valved conduit (VC). The CC analysis shows that 80 % of patients with PA/VSA type A demand transannular patch RVOT with implantation autologous pericardial monocusp or monocusp membrane PTFE (Gore-Tex). Autologous implantation of pericardial VC yields good remote results.
